Lymphangiomas: Rare presentations in oral cavity and scrotum in pediatric age group

Area of Science:

• Pediatric Surgery
• Dermatology
• Medical Genetics

Background:

• Lymphangiomas are congenital benign tumors with an incidence of 1.2 to 2.8 per 1000 newborns.
• They commonly present at birth or before two years of age, predominantly affecting the head and neck region (50%-70%).

Observation:

• The buccal mucosa is the second most frequent site for lymphangioma, with 14 reported cases, following the anterior two-thirds of the tongue.
• The scrotum is an exceptionally rare site, with fewer than 50 cases reported globally as of 2002.
• This study details two rare cases: a primary, late-onset buccal lymphangioma with vesicular presentation and a genital lymphangioma involving the scrotum, thigh, and groin.

Findings:

• The presented cases underscore the variability in lymphangioma presentation, including unusual locations and late-onset occurrences.
• The management of lymphangioma often requires a multidisciplinary approach due to potential involvement of vital structures and functional/aesthetic concerns.

Implications:

• Understanding the diverse clinical spectrum of lymphangioma is crucial for accurate diagnosis and timely intervention.
• These rare case reports contribute to the existing literature, aiding clinicians in managing atypical lymphangioma presentations.
• Further research into the etiology and optimal treatment strategies for rare lymphangioma variants is warranted.