Pediatric primary synovial chondromatosis of the shoulder, biceps tendon sheath and subcoracoid bursa

J-J Sinikumpu1, S-P Sinikumpu2, K Sirniö3

  • 1Department of Pediatric Surgery and Orthopaedics, PEDEGO Research Center and MRC Oulu, University of Oulu and Oulu University Hospital, Oulu, Finland.

Insights

A rare case of primary synovial chondromatosis in a 14-year-old is presented, highlighting shoulder pain and a palpable mass. This condition involves joint nodules and requires surgical removal with follow-up due to recurrence risk.

Area of Science:

  • Orthopedics
  • Pediatric Rheumatology
  • Musculoskeletal Pathology

Background:

  • Primary synovial chondromatosis is a rare condition characterized by the formation of cartilaginous nodules within synovial joints, tendon sheaths, or bursae.
  • While typically affecting large joints in adults, its occurrence in the pediatric population, particularly in the shoulder, is exceptionally uncommon.

Observation:

  • This report details a 14-year-old patient presenting with shoulder pain and a significant palpable mass, with no history of trauma.
  • Clinical findings, advanced imaging, surgical intervention, and histological analysis confirmed primary synovial chondromatosis involving the glenohumeral joint, biceps tendon sheath, and subcoracoid bursa.

Findings:

  • The condition manifested as multiple calcified nodules, leading to symptoms of pain and a palpable mass.
  • Surgical management involved the removal of loose bodies and synovectomy, performed via open and arthroscopic-assisted techniques.

Implications:

  • This case underscores the importance of considering rare diagnoses like primary synovial chondromatosis in pediatric patients with unexplained joint masses and pain.
  • Prompt diagnosis and surgical intervention are crucial, with long-term follow-up recommended due to the potential for recurrence and malignant transformation.

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