Is two-staged repair for truncus arteriosus type A3 unpractical?
Shinya Yokoyama1, Ryohei Fukuba1, Kazuhiro Mitani1
1Surgery Division, Congenital Heart Disease Center, Nara Medical University, Kashihara, Japan.
Journal of Cardiac Surgery
|March 3, 2020
Summary
This study presents a two-stage surgical repair for a rare congenital heart defect, persistent truncus arteriosus, in an infant with complex associated anomalies. The approach ensured excellent hemodynamic status post-operation.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Surgery
- Medical Case Study
Background:
- Persistent truncus arteriosus (PTA) is a rare congenital heart defect requiring tailored surgical strategies.
- Complex PTA cases, especially with additional anomalies, pose significant surgical challenges.
Observation:
- A case report of an infant with PTA, right aortic arch, anomalous pulmonary artery branching, and left superior vena cava.
- The infant presented with a complex cardiac malformation necessitating a multi-stage surgical intervention.
Findings:
- A two-stage surgical repair was successfully performed, involving initial bilateral pulmonary arterial banding followed by Rastelli-type definitive repair.
- The surgical strategy successfully reconstructed the right ventricular outflow tract and unified pulmonary arteries, accommodating the left superior vena cava.
Implications:
- A staged surgical approach can be effective for complex cases of persistent truncus arteriosus in infants.
- This strategy offers a viable option for managing intricate congenital heart malformations, leading to positive patient outcomes.


