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Defects in Galactose Metabolism and Glycoconjugate Biosynthesis in a UDP-Glucose Pyrophosphorylase-Deficient Cell

Christelle Durrant1, Jana I Fuehring2, Alexandra Willemetz1

  • 1INSERM U1149, Université de Paris, 16 rue Henri Huchard, 75018 Paris, France.

International Journal of Molecular Sciences
|March 20, 2020
PubMed

Keywords:
UDP-galactoseUDP-glucoseUGP2congenital disorders of glycosylation (CDGs)developmental epileptic encephalopathies (DEEs)galactoseglycosphingolipidprion proteinprotein glycosylation

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