Intramural Bronchogenic Cysts in the Pediatric Population

Sharif Almatrafi1

  • 1Otorhinolaryngology, Head & Neck Surgery, College of Medicine, Prince Sattam Bin Abdulaziz University, Riyadh-Al Kharj, SAU.

Cureus
|April 8, 2020
PubMed

Insights

Intramural bronchogenic cysts are rare congenital malformations in children. Surgical excision is the recommended treatment, but more research on managing complications is needed.

Area of Science:

  • Pediatric Surgery
  • Congenital Malformations
  • Thoracic Surgery

Background:

  • Bronchogenic cysts are rare congenital malformations arising from the tracheobronchial tree.
  • Intramural variants are particularly uncommon, presenting diagnostic and therapeutic challenges.
  • Fatal complications can occur, especially in neonates and infants.

Purpose of the Study:

  • To review and synthesize existing literature on intramural bronchogenic cysts in pediatric patients.
  • To evaluate the clinical manifestations, diagnostic approaches, and management strategies.
  • To highlight the importance of considering this rare condition in differential diagnoses.

Main Methods:

  • A systematic literature search was conducted across major medical databases.
  • Articles published between 2000 and 2020 were screened for eligibility.
  • Eight relevant studies were included in this review based on predefined criteria.

Main Results:

  • Intramural bronchogenic cysts are rare but significant pediatric conditions.
  • Diagnosis can be challenging due to the rarity and varied presentations.
  • Surgical excision is the current standard of care for these cysts.

Conclusions:

  • Intramural bronchogenic cysts require careful consideration in pediatric differential diagnoses.
  • Prompt surgical intervention is crucial for favorable outcomes.
  • Further research is warranted to address the management of associated complications.

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