Ectopic pancreas and cystic fibrosis

K P Dawson1

  • 1Christchurch School of Medicine, NZ.

Australian and New Zealand Journal of Medicine
|October 1, 1988
PubMed

Insights

A rare case of infant cystic fibrosis presented with duodenal obstruction. Surgery successfully resolved the obstruction caused by an ectopic pancreas.

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Genetics

Background:

  • Cystic fibrosis is a genetic disorder affecting multiple organs.
  • Duodenal obstruction is a serious complication in infants.
  • Ectopic pancreas can cause gastrointestinal issues.

Observation:

  • An infant diagnosed with cystic fibrosis experienced duodenal obstruction.
  • The obstruction was located in the third part of the duodenum.

Findings:

  • The duodenal obstruction was caused by a submucosal ectopic pancreas.
  • Surgical intervention successfully relieved the obstruction.

Implications:

  • Highlights the importance of considering ectopic pancreas in CF infants with duodenal obstruction.
  • Demonstrates surgical efficacy in managing this rare complication.
  • Contributes to understanding CF-related gastrointestinal manifestations.

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