Juvenile dermatomyositis presenting as complete heart block in a 10-year-old girl

Ritwik Ghosh1, Devlina Roy1, Souvik Dubey2

  • 1Department of General Medicine, Burdwan Medical College & Hospital , Burdwan, India.

Insights

Juvenile dermatomyositis (JDM) can cause heart problems like complete heart block. Early detection and corticosteroid treatment are crucial for managing cardiac issues in JDM patients.

Area of Science:

  • Pediatric Rheumatology
  • Cardiology

Background:

  • Juvenile dermatomyositis (JDM) is an autoimmune disease impacting muscles and skin.
  • Cardiac involvement, including conduction abnormalities and myocardial dysfunction, is a known complication of JDM.
  • Cardiac manifestations in JDM can appear anytime, from disease onset to long-term follow-up, necessitating regular screening.

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