Adults forms of scimitar syndrome

Area of Science:

• Cardiology
• Thoracic Surgery
• Medical Imaging

Background:

• Scimitar syndrome is a rare congenital heart defect characterized by anomalous pulmonary venous return from the right lung.
• The condition involves the right pulmonary veins draining into the inferior vena cava instead of the left atrium.
• Severe cases are typically diagnosed in infancy or childhood, while milder forms may remain asymptomatic in adults.

Observation:

• This report presents two adult cases of Scimitar syndrome.
• One patient presented with chest discomfort, a less common symptom in adults with this condition.
• The diagnosis in adults is often incidental or delayed due to the subtle presentation.

Findings:

• Adult-onset Scimitar syndrome can present with varied symptoms, including chest discomfort.
• Mild forms of anomalous pulmonary venous return may not manifest until adulthood.
• Diagnostic imaging, such as echocardiography and CT pulmonary angiography, is crucial for identification.

Implications:

• Increased awareness of Scimitar syndrome in adults is necessary for timely diagnosis and management.
• Early recognition can prevent potential complications associated with undiagnosed anomalous pulmonary venous return.
• Further research into the long-term outcomes and optimal treatment strategies for adult Scimitar syndrome is warranted.