[Orbital schwannoma in a child with acute proptosis]

Area of Science:

• Neuro-oncology
• Ophthalmology
• Pediatric Oncology

Background:

• Schwannomas are typically benign tumors arising from Schwann cells, which form the myelin sheath of peripheral nerves.
• While common in the intracranial space, orbital schwannomas are rare, particularly in pediatric patients, accounting for less than 10% of intracranial tumors.
• This case focuses on the diagnostic and therapeutic challenges of a rare pediatric orbital schwannoma.

Observation:

• A previously healthy 6-year-and-11-month-old patient presented with intermittent headaches, proptosis, decreased vision in the left eye, epiphora, and strabismus.
• Radiological imaging revealed a retro-orbital mass.
• The patient underwent surgical resection of the mass.

Findings:

• The resected mass was diagnosed as an orbital schwannoma through anatomopathological examination.
• The tumor was completely removed macroscopically.
• This confirms the diagnosis and successful surgical outcome.

Implications:

• This case underscores the importance of considering schwannomas in the differential diagnosis of pediatric orbital masses, despite their rarity.
• Early diagnosis and complete surgical excision are crucial for favorable outcomes in pediatric orbital schwannomas.
• Further research into the specific characteristics and management of pediatric orbital schwannomas may improve clinical practice.