Bronchial varices in a child with tricuspid atresia six years post Fontan correction

Shreya Bhushan1, Vikas Goyal1, Cameron Ward2

  • 1Department of Respiratory and Sleep Medicine Queensland Children's Hospital Brisbane QLD Australia.

Insights

Bronchial varices, rare in children, can occur after Fontan procedures. Embolization may resolve hemoptysis but not always the varices themselves.

Area of Science:

  • Pediatric Cardiology
  • Vascular Pathology
  • Interventional Pulmonology

Background:

  • Tracheal and bronchial varices are uncommon in pediatric populations.
  • These vascular anomalies are typically associated with adult conditions like Fontan circulation failure, portal hypertension, or pulmonary hypertension.

Observation:

  • A case of hemoptysis and bronchial varices is presented in a child six years post-Fontan procedure for tricuspid atresia.
  • Imaging revealed tortuous mediastinal and transpleural arterial collaterals.

Findings:

  • The child underwent successful embolization of the identified arterial collaterals.
  • Post-embolization, hemoptysis resolved, but bronchial varices persisted upon repeat bronchoscopy.

Implications:

  • This case highlights the potential for bronchial varices post-Fontan procedure in children.
  • While embolization can manage hemoptysis, persistent varices may require further monitoring or management strategies.