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Anesthetic implications of a pediatric patient with stiff skin syndrome: A case report

Edgar E Kiss1,2, Gijo Alex1,2, Neethu Chandran1,2

  • 1Department of Anesthesiology and Pain Management, University of Texas Southwestern, Dallas, TX, USA.

Paediatric Anaesthesia
|August 8, 2020
PubMed

Insights

Stiff skin syndrome presents unique anesthetic challenges in pediatric patients due to inflexible skin and limited joint mobility. Careful planning is crucial for safe intubation, ventilation, and positioning during surgery.

Area of Science:

  • Anesthesiology
  • Genetics
  • Pediatrics

Background:

  • Stiff skin syndrome (SSS) is a rare genetic disorder presenting in infancy or early childhood.
  • Characterized by generalized skin ossification, leading to significant joint mobility limitations.
  • These physical limitations pose considerable challenges for anesthetic management.

Keywords:
airwaychilddifficultgeneral anesthesiainduction of anesthesiastiff skin syndrome

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