Quality improvement initiative to improve pulmonary function in pediatric cystic fibrosis patients

Amy G Filbrun1, Catherine Enochs1, Lindsay Caverly1

  • 1Department of Pediatrics, Division of Pediatric Pulmonology, University of Michigan, Ann Arbor, Michigan.

Pediatric Pulmonology
|August 10, 2020
PubMed

Insights

A quality improvement project in Cystic Fibrosis (CF) patients improved lung function. Standardized care plans and patient education led to a significant increase in forced expiratory volume in 1-second (FEV1) percent predicted.

Area of Science:

  • Pulmonology
  • Pediatric Medicine
  • Quality Improvement Science

Background:

  • Cystic Fibrosis (CF) affects lung function, necessitating interventions to improve outcomes.
  • Quality Improvement (QI) projects are crucial for enhancing patient care in chronic diseases like CF.
  • Maintaining optimal lung function, measured by forced expiratory volume in 1-second (FEV1) percent predicted (pp), is a key goal in CF management.

Purpose of the Study:

  • To implement a QI project aimed at increasing the mean FEV1 pp by 5% in 12 months for pediatric CF patients (6-21 years) with FEV1 pp ≤ 80%.
  • To identify and address barriers to adherence and lung function decline in young CF patients.
  • To standardize care delivery across providers for individualized patient treatment plans.

Main Methods:

  • Utilized cause and effect diagrams (fishbones) to identify factors contributing to suboptimal FEV1 pp.
  • Developed flowcharts to systematically address identified barriers to treatment adherence and lung function improvement.
  • Implemented a standardized, individualized care approach for CF patients with FEV1 pp ≤ 80%.

Main Results:

  • The project identified a need for enhanced patient/family education and consistent treatment plan delivery at clinic visits.
  • After 6 months, mean FEV1 pp improved by 6.4% (CI, 0.4%-12.9%).
  • At 12 months, mean FEV1 pp improved by 14% (CI, 6.5%-21.4%), significantly exceeding the 5% goal.

Conclusions:

  • A collaborative QI approach involving healthcare teams, patients, and families can effectively improve lung function in pediatric CF patients.
  • Standardized care pathways and individualized treatment plans are effective in overcoming barriers to improved FEV1 pp.
  • This QI initiative demonstrated a successful strategy for enhancing respiratory health outcomes in young individuals with Cystic Fibrosis.
Abstract

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