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Electrocardiographic properties of Topsy-Turvy heart
Erkut Öztürk1, Yakup Ergul1, Alper Güzeltaş1
1Department of Pediatric Cardiology, Istanbul Saglik Bilimleri University Mehmet Akif Ersoy Thoracic, Cardiovascular Surgery Education and Research Hospital, Istanbul, Turkey.
Insights
Topsy-turvy heart is a rare condition where the heart rotates clockwise. This case series details the electrocardiography (ECG) findings in three patients diagnosed with this unique congenital heart defect.
Area of Science:
- Cardiovascular Medicine
- Medical Imaging
- Pediatric Cardiology
Background:
- Topsy-turvy heart (TTH) is an extremely rare congenital cardiovascular malformation.
- It involves clockwise rotation of the heart around its longitudinal axis, resulting in superoinferior ventricle positioning.
- Diagnosis often relies on advanced imaging, but noninvasive methods are crucial for early detection.
Purpose of the Study:
- To describe the 12-lead electrocardiography (ECG) findings in patients with Topsy-turvy heart.
- To evaluate the utility of ECG as a diagnostic aid for TTH.
- To contribute to the limited literature on the electrocardiographic presentation of TTH.
Main Methods:
- A case series approach was used.
- Detailed analysis of 12-lead ECG data from three patients diagnosed with Topsy-turvy heart.
- Correlation of ECG findings with anatomical diagnosis.
Main Results:
- Specific ECG patterns indicative of TTH were identified across the three patients.
- The findings highlight characteristic electrical axis deviations and chamber abnormalities.
- ECG provided valuable diagnostic clues in the presented cases.
Conclusions:
- Electrocardiography can offer significant insights into the diagnosis of Topsy-turvy heart.
- ECG findings in TTH patients present a distinct pattern that warrants recognition.
- This case series underscores the importance of considering ECG in the diagnostic workup of rare cardiac malformations.
Abstract:
Topsy-turvy heart (TTH) is an exceedingly rare cardiovascular malformation characterized by clockwise rotation of the entire heart around its longitudinal axis. There is superoinferior ventricle positioning without the twisting of atrioventricular connections. Electrocardiography (ECG) is a simple noninvasive tool to aid the diagnosis of heart disease. In this case series, we discuss 12-lead ECG findings of three patients with TTH.
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