Electrocardiographic properties of Topsy-Turvy heart

Erkut Öztürk1, Yakup Ergul1, Alper Güzeltaş1

  • 1Department of Pediatric Cardiology, Istanbul Saglik Bilimleri University Mehmet Akif Ersoy Thoracic, Cardiovascular Surgery Education and Research Hospital, Istanbul, Turkey.

Insights

Topsy-turvy heart is a rare condition where the heart rotates clockwise. This case series details the electrocardiography (ECG) findings in three patients diagnosed with this unique congenital heart defect.

Area of Science:

  • Cardiovascular Medicine
  • Medical Imaging
  • Pediatric Cardiology

Background:

  • Topsy-turvy heart (TTH) is an extremely rare congenital cardiovascular malformation.
  • It involves clockwise rotation of the heart around its longitudinal axis, resulting in superoinferior ventricle positioning.
  • Diagnosis often relies on advanced imaging, but noninvasive methods are crucial for early detection.

Purpose of the Study:

  • To describe the 12-lead electrocardiography (ECG) findings in patients with Topsy-turvy heart.
  • To evaluate the utility of ECG as a diagnostic aid for TTH.
  • To contribute to the limited literature on the electrocardiographic presentation of TTH.

Main Methods:

  • A case series approach was used.
  • Detailed analysis of 12-lead ECG data from three patients diagnosed with Topsy-turvy heart.
  • Correlation of ECG findings with anatomical diagnosis.

Main Results:

  • Specific ECG patterns indicative of TTH were identified across the three patients.
  • The findings highlight characteristic electrical axis deviations and chamber abnormalities.
  • ECG provided valuable diagnostic clues in the presented cases.

Conclusions:

  • Electrocardiography can offer significant insights into the diagnosis of Topsy-turvy heart.
  • ECG findings in TTH patients present a distinct pattern that warrants recognition.
  • This case series underscores the importance of considering ECG in the diagnostic workup of rare cardiac malformations.

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