An interventricular membranous septal aneurysm obstructing the right ventricle outflow tract in a five-year-old boy:

Lubna Bakr1, Mohammad Al-Jadaan2, Mohammad Younes2

  • 1Department of Cardiac Surgery, Faculty of Medicine, Damascus University, Damascus, Syria. lubna-bakr@hotmail.com.

Abstract

Insights

A rare aneurysm of the membranous septum caused dynamic right ventricular outflow tract obstruction in a child. Surgical resection resolved the stenosis, highlighting a critical diagnosis for pediatric dyspnea.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Aneurysms of the membranous septum (AVS) are uncommon cardiac malformations.
  • Obstruction of the right ventricular outflow tract (RVOT) by AVS is exceptionally rare, with only 11 cases reported since 1982.

Observation:

  • A five-year-old boy presented with congenital dyspnea.
  • Transthoracic echocardiography revealed a large aneurysm of the membranous septum impinging on the RVOT, causing significant stenosis.

Findings:

  • The case represents the second reported instance of dynamic RVOT obstruction due to a membranous ventricular septal aneurysm in a pediatric patient.
  • Surgical resection of the aneurysmal tissue successfully treated the RVOT stenosis.

Implications:

  • This case underscores the importance of considering AVS as a cause of RVOT obstruction in children with unexplained dyspnea.
  • Further research is warranted to fully elucidate the pathophysiology and clinical spectrum of AVS.

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