Outcomes of biventricular repair for shone's complex

Ahmed F Elmahrouk1,2, Mohamed F Ismail1,3, Amr A Arafat2

  • 1Division of Cardiac Surgery, Department of Cardiovascular, King Faisal Specialist Hospital and Research Center, Jeddah, Saudi Arabia.

Insights

Biventricular repair for Shone's complex shows good outcomes, with significant growth observed in the mitral valve (MV) and left ventricular outflow tract (LVOT) post-surgery. Reoperation is common, particularly with associated aortic valve issues.

Area of Science:

  • Pediatric Cardiology
  • Congenital Heart Disease
  • Cardiac Surgery

Background:

  • Shone's complex is a rare congenital heart defect involving the mitral valve (MV) and left ventricular outflow tract (LVOT).
  • This condition necessitates complex surgical intervention for optimal outcomes.

Purpose of the Study:

  • To evaluate the outcomes of biventricular repair in patients with Shone's complex.
  • To assess the growth of the MV, aortic valve, and LVOT post-repair.
  • To determine long-term survival rates and identify factors influencing reoperation.

Main Methods:

  • Retrospective analysis of patients diagnosed with Shone's complex undergoing biventricular repair.
  • Collection of data on patient characteristics, MV lesions, and associated anomalies.
  • Regular echocardiographic follow-up to monitor MV, aortic valve, and LVOT z-scores.

Main Results:

  • Thirty-seven patients were included; 30.6% had pulmonary hypertension.
  • Coarctation repair was the most common initial procedure (70%).
  • Survival rates at 1, 5, and 10 years were 94.4%, 90%, and 76.9%, respectively. Reoperation was required in 13 patients, associated with aortic valve lesions. Significant growth was noted in MV (0.35/year) and LVOT (0.53/year) z-scores.

Conclusions:

  • Biventricular repair offers favorable outcomes for Shone's complex.
  • Reoperation is frequently necessary, especially in cases with low aortic valve z-scores.
  • Post-repair, the MV and LVOT demonstrate substantial growth, indicating successful surgical management.
Abstract

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