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Published on: July 18, 2014
Outcomes of biventricular repair for shone's complex
Ahmed F Elmahrouk1,2, Mohamed F Ismail1,3, Amr A Arafat2
1Division of Cardiac Surgery, Department of Cardiovascular, King Faisal Specialist Hospital and Research Center, Jeddah, Saudi Arabia.
Insights
Biventricular repair for Shone's complex shows good outcomes, with significant growth observed in the mitral valve (MV) and left ventricular outflow tract (LVOT) post-surgery. Reoperation is common, particularly with associated aortic valve issues.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Cardiac Surgery
Background:
- Shone's complex is a rare congenital heart defect involving the mitral valve (MV) and left ventricular outflow tract (LVOT).
- This condition necessitates complex surgical intervention for optimal outcomes.
Purpose of the Study:
- To evaluate the outcomes of biventricular repair in patients with Shone's complex.
- To assess the growth of the MV, aortic valve, and LVOT post-repair.
- To determine long-term survival rates and identify factors influencing reoperation.
Main Methods:
- Retrospective analysis of patients diagnosed with Shone's complex undergoing biventricular repair.
- Collection of data on patient characteristics, MV lesions, and associated anomalies.
- Regular echocardiographic follow-up to monitor MV, aortic valve, and LVOT z-scores.
Main Results:
- Thirty-seven patients were included; 30.6% had pulmonary hypertension.
- Coarctation repair was the most common initial procedure (70%).
- Survival rates at 1, 5, and 10 years were 94.4%, 90%, and 76.9%, respectively. Reoperation was required in 13 patients, associated with aortic valve lesions. Significant growth was noted in MV (0.35/year) and LVOT (0.53/year) z-scores.
Conclusions:
- Biventricular repair offers favorable outcomes for Shone's complex.
- Reoperation is frequently necessary, especially in cases with low aortic valve z-scores.
- Post-repair, the MV and LVOT demonstrate substantial growth, indicating successful surgical management.
Background:
Shone's complex is a rare lesion affecting the mitral valve (MV) and left ventricular outflow tract (LVOT). The objective of this study is to report the outcomes after Shone's complex repair, the growth of mitral and aortic valve and LVOT, and long-term survival.
Methods:
This retrospective study included all patients diagnosed with Shone's complex, who underwent biventricular repair. Data including patients' characteristics, type of the MV lesion and the associated lesions were collected. Patients were followed up regularly with echocardiography, and the changes in mitral and aortic valve z-score and LVOT z-score were recorded.
Results:
Thirty-seven patients were included in the study, the median age was 3.4 months, and 11 patients (30.6%) had pulmonary hypertension. The main procedure performed during the first surgical intervention was coarctation repair in 26 patients (70%). Twelve patients had MV repair, and five had MV replacement. Operative mortality occurred in 1 patient (2.7%), median follow up was 52 (25-75th percentile: 22-84) months. Survival at 1, 5, and 10 years was 94.4%, 90%, and 76.9%, respectively. Reoperation was required in 13 patients, mainly for LVOT repair (n = 8). Reoperation was significantly associated with associated aortic valve lesion (p = .044). The growth of the MV z-score was 0.35 per year; p < .001, aortic valve z-score 0.086 per year; p = 0.422, and the LVOT z-score was 0.53 per year; p = .01.
Conclusion:
Biventricular repair of Shone's complex has good outcomes. Reoperation is frequently encountered, especially with low aortic valve z-score. The MV and LVOT have significant growth following Shone's complex repair.
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