Infantile dilated cardiomyopathy due to congenital left main coronary ostial stenosis
Jacqueline Doyle1, Tammy Churchill1, Shahryar M Chowdhury1
1Department of Paediatrics, Division of Paediatric Cardiology, Medical University of South Carolina, Charleston, SC, USA.
Insights
Congenital heart disease can manifest as infant heart failure. This case highlights left coronary ostial stenosis as a cause of dilated cardiomyopathy in an infant.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Cardiovascular Medicine
Background:
- Congenital heart anomalies are a rare cause of heart failure in infants.
- Anomalous left coronary artery from the pulmonary artery is the most common coronary anomaly presenting as heart failure.
- Other coronary artery abnormalities can also mimic common presentations of heart failure.
Purpose of the Study:
- To report a case of left coronary ostial stenosis presenting as dilated cardiomyopathy in an infant.
- To emphasize the importance of considering coronary artery anomalies in the differential diagnosis of infant heart failure.
Main Methods:
- Case report presentation.
- Review of clinical presentation, diagnostic workup, and management.
Main Results:
- The infant presented with symptoms of heart failure.
- Diagnostic imaging revealed left coronary ostial stenosis.
- The stenosis was identified as the cause of dilated cardiomyopathy.
Conclusions:
- Left coronary ostial stenosis is a critical diagnosis in infants presenting with heart failure.
- Prompt recognition and management of coronary artery anomalies are essential for favorable outcomes in affected infants.
Abstract:
Although a rare form of congenital heart disease, anomalies of the coronary arteries can present as heart failure in infants. The most common lesion is an anomalous left coronary artery arising from the pulmonary artery, but other abnormalities can present similarly. This case is an infant who is found to have left coronary ostial stenosis causing dilated cardiomyopathy.
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