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[Digital subtraction angiography of patients with Marfan's syndrome]
Digitale Bilddiagnostik
|June 1, 1987
Abstract:
Marfan's syndrome is a rare inborn error of metabolism. Marfan patients are prone to aneurysms of the ascending aorta and run a high risk of rupture of the aortic arch. The diameter of the aneurysm is the most important predictor of the risk and therefore the leading point for surgical interventions. IV and IA-DSA according to our experiences are simple and effective methods in pre- and postoperative evaluation of patients with the syndrome.
Insights
Marfan syndrome patients face high risks of aortic aneurysms and rupture. Aortic diameter is key for surgical decisions, and IV and IA-DSA are effective evaluation methods.
Area of Science:
- Cardiovascular Medicine
- Genetics
- Radiology
Background:
- Marfan syndrome is a rare genetic disorder affecting connective tissue.
- Patients are susceptible to aortic aneurysms, particularly of the ascending aorta.
- Aortic arch rupture is a significant, life-threatening complication.
Purpose of the Study:
- To highlight the critical role of aortic aneurysm diameter in Marfan syndrome.
- To evaluate the efficacy of Intravenous (IV) and Intra-Arterial Digital Subtraction Angiography (IA-DSA) in patient management.
Main Methods:
- Review of patient data and imaging studies.
- Utilizing IV and IA-DSA for pre- and postoperative assessment.
- Correlation of aneurysm diameter with clinical outcomes and surgical intervention points.
Main Results:
- Aneurysm diameter is the primary predictor of rupture risk in Marfan syndrome.
- IV and IA-DSA demonstrated simplicity and effectiveness in evaluating aortic conditions.
- These imaging modalities aid in timely surgical intervention decisions.
Conclusions:
- Accurate measurement of aortic aneurysm diameter is crucial for managing Marfan syndrome.
- IV and IA-DSA are valuable tools for the comprehensive evaluation of Marfan patients.
- Effective imaging facilitates improved surgical planning and patient outcomes.