Giant choroid plexus cysts with calvarial erosion: a case report and literature review

Runze Yang1, Han Yan2,3, Michael C Dewan4

  • 1Cumming School of Medicine, University of Calgary, Calagary, Canada.

Insights

Giant choroid plexus cysts are rare in children and can cause symptoms like increased head circumference. Surgical removal of this giant cyst led to an excellent recovery in a 15-month-old boy.

Area of Science:

  • Pediatric Neurosurgery
  • Developmental Neurobiology
  • Cystic Lesions of the Brain

Background:

  • Choroid plexus cysts (CPCs) are intraventricular formations that are typically asymptomatic.
  • Large or giant CPCs are exceptionally rare in the pediatric population, posing diagnostic and management challenges.

Observation:

  • A 15-month-old male presented with macrocephaly and a left parietal bony deformity.
  • Imaging revealed a giant choroid plexus cyst causing significant mass effect.

Findings:

  • The patient underwent successful open resection of the giant choroid plexus cyst.
  • Histopathological analysis confirmed the diagnosis of a choroid plexus cyst.

Implications:

  • This case highlights the importance of considering giant CPCs in the differential diagnosis of pediatric intraventricular masses.
  • Surgical intervention can be highly effective for symptomatic giant CPCs, leading to favorable outcomes.

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