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Cystic fibrosis in adults: diagnosis and management

S Murphy1

  • 1Department of Pediatrics, University of New Mexico School of Medicine, Albuquerque.

Clinics in Chest Medicine
|December 1, 1987
PubMed

Insights

Cystic fibrosis (CF) is increasingly affecting adolescents and adults, requiring updated management strategies. This review covers complications, treatment approaches, and emerging research for older CF patients.

Area of Science:

  • Pulmonology and Genetics
  • Pediatrics and Adult Medicine

Background:

  • Cystic fibrosis (CF) was historically viewed as a pediatric condition.
  • Advances in treatment have led to increased survival, with a growing adult population.

Observation:

  • CF complications like hemoptysis, pneumothorax, sinusitis, pancreatic deficiency, and intestinal obstruction are prevalent in older patients.
  • Clinical evaluation, follow-up, and treatment require tailored approaches for adolescents and adults.

Findings:

  • The review details common CF complications in older individuals.
  • It provides practical guidance for clinicians managing adolescent and adult CF patients.

Implications:

  • Highlights the evolving demographic of cystic fibrosis, necessitating specialized care for adults.
  • Emphasizes the need for ongoing research into CF genetics, its basic defect, and advanced therapies like heart-lung transplantation.

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