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Successful treatment of a child with Schwartz-Jampel syndrome using rapid maxillary expansion and CPAP
Supakit Peanchitlertkajorn1, Thanate Assawakawintip1, Mevadee Pibulniyom2
1Department of Orthodontics, Faculty of Dentistry, Mahidol University, Bangkok, Thailand.
Study Objectives:
We reported an 8-year-old male patient with Schwartz-Jampel syndrome, severe obstructive sleep apnea, constricted maxilla and moderate tonsillar hypertrophy. The syndrome is characterized by myotonia, skeletal dysplasia, and facial dysmorphism.
Methods:
CPAP was initially prescribed, but he was not able to tolerate due to a high pressure setting. Rapid maxillary expansion alone reduced AHI to 10.4 events/h.
Results:
When combined with CPAP, AHI is further reduced to 2.4 events/h. The patient has a better compliance with CPAP following rapid maxillary expansion therapy as the pressure setting decreased.
Conclusions:
This is the first report utilizing a combination of rapid maxillary expansion and CPAP therapy to successfully treat severe pediatric OSA.
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