Cardiac Lipomatosis: A Rare Form of Left Ventricular Hypertrophy

Mateusz Śpiewak1, Mariusz Kłopotowski2, Łukasz A Małek3

  • 1Magnetic Resonance Unit, Department of Radiology, National Institute of Cardiology, Warsaw, Poland.

Insights

A 30-year-old female presented with abnormal ECG findings of left ventricular hypertrophy. Cardiac imaging revealed atypical wall thickening with fat-like signal intensity, showing no progression over time.

Area of Science:

  • Cardiology
  • Cardiovascular Imaging
  • Cardiac MRI

Background:

  • Left ventricular hypertrophy (LVH) is a common finding on electrocardiography (ECG).
  • Atypical patterns of LVH can present diagnostic challenges.
  • Cardiac magnetic resonance (CMR) is crucial for detailed cardiac structure assessment.

Observation:

  • A 30-year-old female with asymptomatic LVH on ECG.
  • Echocardiography showed heterogeneous echogenicity in left ventricular walls.
  • Cardiac MRI revealed marked, symmetrical ventricular wall thickening.

Findings:

  • The thickened ventricular walls demonstrated increased signal intensity on MRI, mimicking subcutaneous fat.
  • No progression of left ventricular hypertrophy was observed on follow-up imaging.
  • This suggests a potential infiltrative or storage process.

Implications:

  • This case highlights the utility of advanced cardiac imaging in diagnosing rare causes of left ventricular hypertrophy.
  • Understanding atypical MRI signal characteristics is vital for accurate diagnosis.
  • Further investigation may be warranted to determine the underlying etiology.

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