Congenitally Corrected Transposition of the Great Arteries at Age 88 Years

Kohei Osakada1, Masanobu Ohya1, Kenji Waki2

  • 1Department of Cardiology, Kurashiki Central Hospital, Kurashiki, Japan.

CJC Open
|December 11, 2020
PubMed

Insights

Congenitally corrected transposition of the great arteries (CCTGA) is a rare heart defect. This case report details the oldest-diagnosed patient at 88 years old, offering insights into long-term prognoses.

Area of Science:

  • Cardiology
  • Medical Case Reports
  • Rare Diseases

Background:

  • Congenital heart disease (CHD) is typically diagnosed in infancy.
  • Some complex CHDs, like congenitally corrected transposition of the great arteries (CCTGA), can remain undiagnosed until adulthood.
  • The long-term prognosis for CCTGA, especially without associated anomalies, is not well-established.

Observation:

  • A case of CCTGA diagnosed at 88 years old is presented.
  • This represents the oldest reported age at diagnosis for CCTGA in medical literature.
  • The patient had CCTGA without frequently associated cardiac anomalies.

Findings:

  • The diagnosis at an advanced age suggests potential for longer survival in select CCTGA cases.
  • This case highlights the possibility of late diagnosis in rare congenital heart conditions.
  • The patient's survival to 88 years provides a data point for understanding CCTGA natural history.

Implications:

  • This case may offer new insights into the prognosis of CCTGA without associated cardiac anomalies.
  • It underscores the importance of considering adult congenital heart disease diagnoses.
  • Further research into long-term outcomes for adult-diagnosed CCTGA is warranted.

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