Treatment of Ruptured Giant Omphalocele and Gastroschisis with Liver Herniation using a Wound Retractor as a Novel

Jana Nelson1, Robin Wachowiak1, Manuela Siekmeyer2

  • 1Division of Pediatric Surgery, Leipzig University Hospital for Children and Adolescents, Leipzig, Saxony, Germany.

Insights

Ruptured giant omphaloceles and gastroschisis pose significant challenges. A staged surgical repair using a wound retractor silo effectively managed these complex cases, allowing for abdominal reduction and closure.

Area of Science:

  • Pediatric Surgery
  • Neonatal Care
  • Congenital Abnormalities

Background:

  • Ruptured giant omphaloceles (GO) and gastroschisis with total liver herniation represent rare, severe congenital abdominal wall defects.
  • These conditions often lead to lethal outcomes due to the complexity of surgical and postsurgical management.

Observation:

  • Two cases of infants with ruptured giant omphaloceles and gastroschisis involving total liver herniation were reported.
  • The infants presented with exceptionally large abdominal wall defects.

Findings:

  • A staged surgical repair technique utilizing a wound retractor as a silo was employed.
  • This method facilitated the reduction of the liver and intestines into the abdominal cavity.

Implications:

  • The described technique allowed for secondary closure of the abdominal cavity within the first 1-2 weeks of life.
  • This approach offers a potential management strategy for complex abdominal wall defects in neonates.
  • Successful management of these rare conditions can improve survival rates in affected infants.

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