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Eyelid reconstruction in pachydermoperiostosis
1Division of Plastic Surgery, Kokura Memorial Hospital, Kitakyushu, Japan.
Plastic and Reconstructive Surgery
|January 1, 1988
Summary
Pachydermoperiostosis, a rare disorder, can cause eyelid thickening and vision issues. Surgical eyelid reduction successfully restored full eye opening and reduced secretions in an affected patient.
Area of Science:
- Dermatology
- Ophthalmology
- Genetics
Background:
- Pachydermoperiostosis (PP) is a rare genetic disorder characterized by a triad of digital clubbing, hypertrophic osteoarthropathy, and skin thickening.
- Ocular manifestations, though less common, can significantly impact quality of life, including eyelid abnormalities.
Observation:
- An unusual case of pachydermoperiostosis presented with severe eyelid enlargement (blepharoptosis), excessive lacrimation, and functional impairment in eye opening.
- The thickened eyelid tissues obstructed vision and caused discomfort due to excessive secretions.
Findings:
- Surgical intervention involving partial and serial excisions of both upper and lower eyelids was performed.
- Post-operative assessment revealed complete restoration of eyelid function, enabling full eye opening.
- A significant reduction in excessive ocular secretions was also noted following the surgical procedures.
Implications:
- This case highlights the potential for surgical correction of severe eyelid deformities in pachydermoperiostosis.
- Ophthalmologists and dermatologists should consider surgical management for functional vision impairment caused by PP-related eyelid changes.
- Early diagnosis and intervention can improve patient outcomes and quality of life in affected individuals.