Spontaneous rupture of a coronary artery fistula presenting with post-exertional syncope and haemopericardium
Manan H Desai1,2, Laura J Olivieri3, Karthik V Ramakrishnan1,4
1Division of Cardiac Surgery, Children's National Hospital, Washington, DC, USA.
Insights
A child with an asymptomatic coronary artery fistula (CAF) experienced a life-threatening rupture, requiring emergency surgery. This case highlights the critical need for vigilance and prompt management of CAF complications.
Area of Science:
- Cardiology
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Coronary artery fistulas (CAFs) are abnormal connections between a coronary artery and a heart chamber or major vessel.
- While often asymptomatic, CAFs can lead to serious complications, including rupture.
Observation:
- An 8-year-old presented with exertional syncope and hemopericardium.
- This was attributed to a contained rupture of a previously asymptomatic coronary artery fistula.
Findings:
- Initial transcatheter closure attempt failed, with the fistula rupturing again.
- Emergency surgical repair was necessitated due to the recurrent rupture.
Implications:
- Spontaneous rupture of CAF is a rare but catastrophic event.
- A high index of suspicion, timely diagnosis, and multidisciplinary team management are crucial for patients with CAF.
Abstract:
An 8-year-old with a known diagnosis of an asymptomatic coronary artery fistula (CAF) presented with exertional syncope and haemopericardium due to contained rupture of CAF. A transcatheter closure was attempted, but the fistula ruptured again prompting emergency surgical repair. Spontaneous rupture is a catastrophic complication of CAF and warrants a high index of suspicion, timely diagnosis and team management.
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