Surgical Single Stage Treatment for Obstructive Hypertrophic Cardiomyopathy and Aortic Arch Aneurysm

Davide Margonato1,2, Valerio Stefano Tolva3, Giuseppe Vaccari4

  • 1Department of Cardiology, Policlinico di Monza, Monza, Italy.

Aorta (Stamford, Conn.)
|December 28, 2020
PubMed

Insights

Obstructive hypertrophic cardiomyopathy and aortic arch aneurysm rarely occur together. This case report details a unique patient successfully treated for both conditions with a single surgical intervention.

Area of Science:

  • Cardiovascular Medicine
  • Cardiac Surgery
  • Vascular Surgery

Background:

  • Obstructive hypertrophic cardiomyopathy (oHCM) presents a significant challenge in cardiac surgery.
  • Severe aortic pathologies, such as aortic arch aneurysms, require complex vascular interventions.
  • The simultaneous occurrence of oHCM and aortic arch pathology is exceptionally rare, posing unique clinical and surgical dilemmas.

Purpose of the Study:

  • To report a unique case of a patient with coexisting obstructive hypertrophic cardiomyopathy and aortic arch aneurysm.
  • To describe the successful management of these two rare conditions through a single surgical procedure.
  • To highlight the feasibility and potential benefits of a combined surgical approach for complex cardiovascular pathologies.

Main Methods:

  • A comprehensive review of the patient's medical history, diagnostic imaging, and surgical records.
  • Detailed description of the surgical technique employed for simultaneous repair of the aortic arch aneurysm and management of obstructive hypertrophic cardiomyopathy.
  • Postoperative assessment of the patient's clinical status and echocardiographic findings.

Main Results:

  • The patient presented with symptomatic obstructive hypertrophic cardiomyopathy and a large aortic arch aneurysm.
  • A single, complex surgical procedure was successfully performed, addressing both pathologies.
  • The patient experienced a favorable postoperative recovery with resolution of symptoms and improved cardiac function.

Conclusions:

  • The coexistence of obstructive hypertrophic cardiomyopathy and aortic arch aneurysm, while rare, can be managed effectively with a tailored, single-stage surgical approach.
  • This case underscores the importance of considering combined pathologies in complex cardiovascular presentations.
  • A multidisciplinary approach involving cardiac and vascular surgeons is crucial for optimizing outcomes in such rare scenarios.

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