Caliceal diverticulum with ureteropelvic junction obstruction in a dysplastic kidney: a pediatric case report

Keiichi Koizumi1, Noboru Oyachi2, Fuminori Numano2

  • 1Department of Pediatric Surgery, Yamanashi Prefectural Central Hospital, 1-1-1 Fujimi, Kofu-shi, Yamanashi, 400-8506, Japan. koizumi72ac@gmail.com.

CEN Case Reports
|January 8, 2021
PubMed

Insights

A rare congenital anomaly, caliceal diverticulum in children, often links to ureteropelvic junction obstruction and renal dysplasia. This case highlights a pediatric patient with these conditions who remained asymptomatic despite decreased renal function.

Area of Science:

  • Pediatric Urology
  • Congenital Anomalies
  • Renal Pathophysiology

Background:

  • Caliceal diverticulum is an uncommon condition in pediatric patients.
  • Its development is frequently linked to ureteropelvic junction malformations and renal dysplasia.
  • These complex congenital disorders require careful evaluation and management in infants.

Observation:

  • A case involving an infant with a left kidney exhibiting a renal cyst and hydronephrosis detected prenatally.
  • Postnatal diagnosis confirmed hydronephrosis secondary to ureteropelvic junction obstruction and a caliceal diverticulum within a dysplastic left kidney.
  • Despite significantly diminished left renal function, the infant remained asymptomatic.

Findings:

  • The infant presented with a complex interplay of ureteropelvic junction obstruction, renal dysplasia, and caliceal diverticulum.
  • Severe reduction in left renal function did not manifest with any clinical symptoms in the patient.
  • Conservative management was chosen due to the absence of symptoms, with ongoing monitoring.

Implications:

  • This case underscores the potential for asymptomatic presentation of complex renal anomalies in infants.
  • It suggests that conservative management may be appropriate for certain pediatric patients with significant renal dysfunction but no symptoms.
  • Further long-term follow-up is essential to monitor the progression and potential late-onset symptoms of such conditions.

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