Image of the Month: Enterocolitis Following a Pull-through for Total Colonic Hirschsprung Disease in a 2-Year-Old Boy

Anisha Apte1, Elise McKenna2, Marc A Levitt1,2,3

  • 1Department of Surgery, The George Washington University School of Medicine and Health Sciences, Washington, District of Columbia, United States.

Insights

This case study discusses a 2-year-old boy with total colonic Hirschsprung disease (HD) who developed enterocolitis after surgery. It highlights evaluating obstructive symptoms in HD patients post-correction.

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Clinical Case Reports

Background:

  • Hirschsprung disease (HD) is a congenital condition affecting the large intestine.
  • Total colonic HD involves the entire colon, necessitating complex surgical management.
  • Early surgical intervention, including ileostomy and pull-through procedures, is common.

Observation:

  • A 2-year-old boy with total colonic HD experienced recurrent enterocolitis post-colectomy and pull-through surgery.
  • The patient presented with obstructive symptoms following the corrective procedure.
  • A key image and quiz format are used to analyze the case.

Findings:

  • Recurrent enterocolitis is a significant complication in patients with total colonic HD after corrective surgery.
  • Obstructive symptoms warrant careful evaluation in the post-operative period.
  • Multifaceted management strategies may be required for complex HD cases.

Implications:

  • This case underscores the importance of vigilant monitoring for enterocolitis in pediatric patients with HD.
  • Early recognition and management of obstructive symptoms are crucial for optimal outcomes.
  • Further research into long-term complications and tailored surgical approaches for total colonic HD is warranted.

Related Concept Videos

Inflammatory Bowel Disease V: Surgical Management01:21

Inflammatory Bowel Disease V: Surgical Management

Surgical interventions for inflammatory bowel disease (IBD), which includes ulcerative colitis and Crohn's disease, are essential in managing symptoms and addressing complications. The selection of surgical procedures is contingent upon the specific conditions and complications that stem from these illnesses.
Here are some common surgical interventions for IBD:
Imaging Studies III: Gastrointestinal Motility Studies and Virtual Colonoscopy01:26

Imaging Studies III: Gastrointestinal Motility Studies and Virtual Colonoscopy

This lesson explores three gastrointestinal imaging techniques: radionuclide testing, colonic transit studies, and virtual colonoscopy.
Radionuclide Testing
Radionuclide testing is a sophisticated medical technique for assessing gastrointestinal motility. It focuses on gastric emptying and colonic transit time. Radioactive markers track the movement of food through the digestive system, providing insights into gastrointestinal disorders.
In gastric emptying studies, a meal's liquid and solid...
Pyloric Obstruction01:11

Pyloric Obstruction

Pyloric obstruction, also referred to as gastric outlet obstruction, is a condition characterized by narrowing or blockage at the pylorus—the muscular valve regulating the flow of stomach contents into the duodenum. When this passage becomes impaired, the stomach cannot effectively empty its contents into the small intestine. This disruption leads to a range of gastrointestinal symptoms, including early satiety, bloating, epigastric pain, postprandial nausea, persistent vomiting, and...
Intestinal Obstruction I: Introduction01:29

Intestinal Obstruction I: Introduction

Intestinal obstruction is a partial or complete blockage of the small or large intestine that disrupts the normal flow of intestinal contents through the lumen. This interruption impairs digestion, absorption, and fluid balance, and may lead to serious complications if not treated promptly.Mechanical ObstructionMechanical obstruction occurs when a physical blockage prevents intestinal contents from passing, arising from within the lumen or the bowel wall, or from external compression.Adhesions,...
Intestinal Obstruction II: Pathophysiology01:07

Intestinal Obstruction II: Pathophysiology

Intestinal obstruction triggers a series of physiological responses, starting with gas and fluid accumulation in the bowel segment proximal to the obstruction, leading to distension. This distended intestine compresses the diaphragm, hindering lung expansion and potentially leading to reduced respiratory effort, atelectasis, and pneumonia.To overcome the blockage, the gut intensifies contractions, causing colicky abdominal pain, nausea, and vomiting, which reduces fluid and food intake and...
Inflammatory Bowel Disease II: Ulcerative Colitis01:20

Inflammatory Bowel Disease II: Ulcerative Colitis

Ulcerative colitis is a chronic inflammatory disorder of the colon characterized by continuous mucosal inflammation that typically begins in the rectum and extends proximally in a uniform pattern. Its pathogenesis involves a complex interplay of genetic predisposition, immune dysregulation, and environmental influences. These factors converge to impair the colon’s epithelial defenses and promote an exaggerated inflammatory response against luminal contents.Breakdown of the Mucosal BarrierA...