Wunderlich Syndrome: Wonder What It Is
Nishita Parmar1, Jonathan Langdon1, Krithica Kaliannan2
1Department of Radiology and Biomedical Imaging, Yale University School of Medicine, New Haven, CT.
Current Problems in Diagnostic Radiology
|January 23, 2021
Summary
Wunderlich syndrome (WS) is spontaneous kidney hemorrhage without trauma. This review details its multimodality imaging, follow-up, and management for better diagnosis and care.
Area of Science:
- Nephrology
- Radiology
- Urology
Background:
- Wunderlich syndrome (WS) involves spontaneous renal or perinephric hemorrhage without trauma.
- It is less common than traumatic or iatrogenic hemorrhage.
- Classic Lenk's triad is rare; most patients present with flank pain.
Purpose of the Study:
- To review the multimodality imaging approach for diagnosing WS.
- To describe optimal follow-up strategies for patients with WS.
- To elaborate on current management options for WS.
Main Methods:
- Review of multimodality imaging techniques for WS.
- Analysis of diagnostic workup and etiology identification.
- Discussion of follow-up protocols and treatment strategies.
Main Results:
- Etiologies of WS are diverse, including neoplasms, vascular disease, and cystic renal disease.
- Initial CT scans may not reveal the underlying cause.
- Multimodality imaging is crucial for accurate diagnosis and management planning.
Conclusions:
- Accurate diagnosis of WS requires a thorough understanding of imaging findings.
- A systematic approach to imaging, follow-up, and management is essential.
- Radiologists and urologists must be familiar with WS for timely intervention.
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