Leiomyoma in a müllerian remnant. A case report

Leiomyomas are a rather common occurrence in the normal uterus. Müllerian dysgenesis, however, occurs in only approximately 1 in 5,000 female births. We found no case reports of leiomyoma arising from a müllerian remnant, as in the case reported here. Surgical management considerations include identification of the blood supply, separation of the mass from the broad ligament and care in identifying the entire length of the ureter. Due to the extreme rarity of leiomyoma in müllerian remnants, it should be considered low on the list of differential diagnoses of pelvic masses in women with müllerian dysgenesis.