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Minimally Invasive Thumb-sized Pterional Craniotomy for Surgical Clip Ligation of Unruptured Anterior Circulation Aneurysms
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Giant Anterior Fontanel Encephalocoele: A Rare Case Report and Review of Literature

Bikash R Behera1, Sanjib Mishra1, Manmath K Dhir1

  • 1Department of Neurosurgery, Srirama Chandra Bhanja Medical College & Hospital, Cuttack, Odisha, India.

Journal of Pediatric Neurosciences
|February 3, 2021
PubMed

Insights

This study reports a rare case of giant anterior fontanel encephalocoele in a neonate. Management of this rare congenital condition is discussed.

Area of Science:

  • Neuroscience
  • Developmental Biology
  • Pediatric Surgery

Background:

  • Encephalocoele is a congenital condition resulting from defective neural tube closure, leading to herniation of brain tissue and meninges through skull defects.
  • Anterior encephalocoeles are more prevalent in Southeast Asia than in Western countries, with fronto-ethmoidal and orbital types being common.
  • Giant encephalocoeles are rare, typically occurring in the occipital region, making giant interfrontal encephalocoeles exceptionally uncommon.

Observation:

  • A rare case of giant anterior fontanel encephalocoele was observed in a 20-day-old neonate.
  • This specific type, a giant interfrontal encephalocoele through a wide anterior fontanel, is exceedingly rare, with only a few prior case reports.
  • The case highlights the extreme rarity of this specific presentation within the spectrum of anterior encephalocoeles.

Findings:

  • The case involved a giant anterior fontanel encephalocoele, a condition with limited documented instances.
  • The study focuses on the diagnostic and therapeutic challenges posed by such a rare congenital malformation.
  • Detailed discussion on the management strategies for this unique presentation is provided.

Implications:

  • This case report contributes to the limited literature on giant anterior fontanel encephalocoeles, aiding future research.
  • Understanding the management of such rare conditions is crucial for improving outcomes in pediatric neurosurgery.
  • The findings underscore the importance of recognizing and addressing rare congenital cranial defects in neonates.

Keywords:
Cranial dysraphismgiant encephalocoelewide anterior fontanel

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