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Case report: Pulmonary artery thrombosis in cyanotic congenital heart disease

Ali Shan1, Suha Zubairi1, Hassan Mirza1

  • 1National Institute of Cardio-Vascular Diseases, Karachi, Pakistan.

Asian Cardiovascular & Thoracic Annals
|February 22, 2021
PubMed

Insights

Pulmonary artery thrombosis is a rare complication in children with cyanotic congenital heart disease. This case highlights a successful surgical intervention for a complex congenital heart defect with extensive pulmonary artery thrombosis.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Cardiovascular Surgery

Background:

  • Cyanotic congenital heart anomalies are known risk factors for thrombosis.
  • Pulmonary artery thrombosis is an uncommon diagnosis in pediatric congenital heart disease.

Observation:

  • An 11-year-old male presented with progressive dyspnea over six months.
  • Diagnosis revealed complex congenital heart disease including double outlet left ventricle, levo-transposition of the great arteries, pulmonary stenosis, and ventricular septal defect.
  • Significant thrombus was found in the main pulmonary artery extending into branch arteries.

Findings:

  • The patient underwent successful surgical treatment involving thromboendarterectomy and a Glenn shunt.
  • The child experienced an uneventful postoperative recovery, indicating the efficacy of the surgical approach.

Implications:

  • This case underscores the importance of considering pulmonary artery thrombosis in pediatric patients with complex cyanotic heart disease presenting with worsening respiratory symptoms.
  • Surgical management, including thromboendarterectomy and shunting procedures, can be effective in treating extensive pulmonary artery thrombosis in this population.
  • Further research into the mechanisms and optimal management strategies for pulmonary artery thrombosis in congenital heart disease is warranted.

Keywords:
Glenn shuntPulmonary artery thrombosiscyanotic congenital heart diseasethromboendarterectomy

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