Double-barrel adult congenital broncho-esophageal fistulae-images

Prakash Joseph1, Birla Roy Gnanamuthu1, Negine Paul1

  • 1Christian Medical College & Hospital, Vellore, India.

Insights

Congenital broncho-oesophageal fistulae (CBEF) are rare foregut anomalies. This report details a unique case of a double CBEF in an adult, highlighting its uncommon presentation and management.

Area of Science:

  • Medical Science
  • Embryology
  • Surgical Science

Background:

  • Congenital broncho-oesophageal fistulae (CBEF) are rare foregut developmental anomalies.
  • These anomalies arise from abnormal embryonic development, specifically the persistent connection between the tracheal bud and foregut.
  • Typically, CBEF manifest in early life with recurrent respiratory infections and failure to thrive.

Purpose of the Study:

  • To report a rare case of congenital double barrel broncho-oesophageal fistula.
  • To highlight the unusual presentation of this anomaly in a middle-aged adult.
  • To emphasize the rarity of double CBEF, with only one prior reported case.

Main Methods:

  • Case presentation of a middle-aged female patient.
  • Review of relevant medical literature on congenital broncho-oesophageal fistulae.
  • Surgical intervention involving fistula division and repair.

Main Results:

  • A congenital double barrel broncho-oesophageal fistula was identified in a middle-aged adult.
  • This represents an exceptionally rare occurrence, with limited precedent in medical literature.
  • The patient's condition required definitive surgical management.

Conclusions:

  • Congenital double barrel broncho-oesophageal fistulae are exceedingly rare, particularly in adults.
  • Early diagnosis and surgical intervention are crucial for effective management.
  • This case underscores the importance of considering rare congenital anomalies even in adult patients.

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