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Arteriovenous malformation with crossed total hemiatrophy: a case report
K Hirata1, S Katayama, K Yamano
1Department of Neurology, Dokkyo University School of Medicine, Tochigi, Japan.
Journal of Neurology
|January 1, 1988
Summary
This case study describes crossed total hemiatrophy, affecting the right face and left body, linked to a right arteriovenous malformation. A pathological auditory response was the sole brainstem indicator potentially associated with facial atrophy.
Area of Science:
- Neurology
- Vascular Malformations
- Neurodevelopmental Disorders
Background:
- Crossed total hemiatrophy is a rare condition characterized by atrophy on the side opposite to the affected brain lesion.
- Arteriovenous malformations (AVMs) are abnormal tangles of blood vessels that can lead to neurological deficits.
Observation:
- A patient presented with crossed total hemiatrophy, involving the right side of the face and the left side of the trunk and extremities.
- Imaging revealed a right precentral to central arteriovenous malformation.
Findings:
- The atrophy of the trunk and extremities was consistent with the contralateral arteriovenous malformation.
- A pathological early auditory response was the only observed brainstem sign potentially linked to the facial atrophy.
Implications:
- This case highlights the complex relationship between vascular malformations and neurological development.
- Further research is needed to understand the specific mechanisms linking brainstem auditory pathways to facial atrophy in crossed hemiatrophy.