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Multiple odontogenic keratocysts in Ehlers-Danlos syndrome: a rare case report
Anna Starzyńska1, Paulina Adamska2, Łukasz Adamski2
1Department of Oral Surgery, Medical University of Gdańsk, 7 Dębinki Street, 80-211, Gdańsk, Poland. ast@gumed.edu.pl.
Background:
An odontogenic keratocyst is a lesion characterized by aggressive and infiltrative growth. The lesion is characterized by the existence of satellite microcysts (microtumours) and frequent recurrence (up to 30%). Ehlers-Danlos syndrome is a condition in which collagen production or its post-translational modifications are affected. Defects in connective tissues cause symptoms, which range from mild joint hypermobility to life-threatening complications.
Case Presentation:
We present an extremely rare case of an 11-year old girl with Ehlers-Danlos syndrome and coexistence of multiple odontogenic keratocysts.
Conclusions:
This case shows mainly atypical or rare association between multiple odontogenic keratocysts and Ehlers-Danlos syndrome.
