Multidisciplinary management of a rare case of mixed total anomalous pulmonary venous connection

Mixed total anomalous pulmonary venous connection (TAPVC) is a extremely rare congenital heart disease.

We report the initial management of a case of Mixed total anomalous pulmonary venous connection associated to right extralobar bronchopulmonary sequestration (BPS).

Mixed TAPVC associated to right extra-lobar BPS was diagnosed at birth in a full-term newborn. At one month of age, the patient underwent embolization of the BPS, complicated by coil entrapment in the right common iliac artery requiring urgent laparotomy. Few days later, the congenital cardiac repair was accomplished uneventfully. At 12-months follow-up, the patient did not have pulmonary hypertension, but presented a moderate stenosis of the right femoral artery, which was effectively treated with anticoagulation therapy.

The multidisciplinary approach allowed a successful treatment of these complex anomalies and the related potential complications.