Anomalous aortic origin of the left main coronary artery associated with arterial compression-Case report
Davi F Tenório1, Leonardo A Miana1, Antonio C de Almeida Barbosa Filho2
1Cardiovascular Surgery Division, Instituto do Coração do Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo (InCor-HCFMUSP), São Paulo, São Paulo, Brazil.
Insights
Anomalous aortic origin of the coronary artery is a rare condition. Surgical correction in a pediatric patient successfully resolved symptoms of shortness of breath and angina.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Pediatric Cardiac Surgery
Background:
- Anomalous aortic origin of the coronary artery (AAOCA) is a rare congenital anomaly.
- It presents with diverse symptoms, often exercise-induced, including chest pain and syncope.
- Advances in cardiac imaging facilitate earlier diagnosis and management.
Observation:
- An 11-year-old female presented with exertional dyspnea, angina, and syncope.
- Holter monitoring revealed nonsustained ventricular tachycardia.
- Coronary angiotomography identified anomalous origin of the left coronary artery from the right aortic cusp with significant external compression.
Findings:
- Surgical correction involved dissecting the left coronary artery, performing coronary arteriotomy, roof ampliation with autologous pericardium, and creating a neo-ostium.
- The patient experienced a satisfactory postoperative recovery.
- The patient remained asymptomatic at 14 months follow-up.
Implications:
- This case highlights successful surgical management of AAOCA in a pediatric patient.
- Early diagnosis and intervention are crucial for favorable outcomes.
- Surgical techniques can effectively restore coronary artery anatomy and alleviate symptoms.
Background:
Anomalous aortic origin of coronary artery is a rare finding, with varied presentation and symptomatology. Increasingly recognized by cardiac imaging, when found it raises questions about the appropriate approach and management.
Case Presentation:
We present a case of an 11-year-old female who presented with episodes of shortness of breath, angina, and syncope during exercise. Further investigation demonstrated episodes of nonsustained ventricular tachycardia on Holter and coronary angiotomography revealed that the left coronary artery had an anomalous origin from the right cusp with initial short intramural segment and significant external compression in its initial course between the aorta and the pulmonary artery. The patient was submitted to surgical correction with dissection of left coronary artery posterior to the pulmonary artery, coronary arteriotomy, roof ampliation with the autologous pericardium, and creation of neo-ostium in aorta. The patient had a satisfactory postoperative recovery, was discharged on the fifth-day post-op, and remains asymptomatic after 14 months of follow-up. Herein we present surgical video and postoperative echo and computed tomography scan.
Related Concept Videos
Aneurysm I: Introduction
Aneurysm II: Clinical Manifestations and Diagnostic Studies
Aortic Regurgitation II: Clinical Features and Diagnostic Tests
Aortic Regurgitation I: Introduction
Coronary Circulation
Coronary circulation begins at the base of the aorta, where two main arteries arise—the left and right coronary arteries. These arteries encircle the heart in the coronary sulcus and supply the...
Thoracic Aorta


