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Auditory testing outcomes with hearing aids in patients with auditory neuropathy spectrum disorder

Firas Sbeih1, Donald M Goldberg2, Sara Liu1

  • 1Cleveland Clinic Foundation, Head and Neck Institute, USA.

American Journal of Otolaryngology
|April 23, 2021
PubMed

Insights

Hearing aids significantly improved auditory skills in children with Auditory Neuropathy Spectrum Disorder (ANSD), as measured by the Infant Toddler-Meaningful Auditory Integration Scale (IT-MAIS) and Ling 6 Sound Test. Further research is needed to explore long-term outcomes.

Area of Science:

  • Audiology
  • Pediatric Otolaryngology
  • Neuroscience

Background:

  • Auditory Neuropathy Spectrum Disorder (ANSD) presents unique challenges in auditory development.
  • Early audiological intervention is crucial for children with ANSD.
  • Hearing aid efficacy in ANSD requires ongoing evaluation.

Purpose of the Study:

  • To assess the impact of hearing aids on audiologic outcomes in pediatric patients diagnosed with ANSD.
  • To evaluate changes in auditory integration and sound detection using the IT-MAIS and Ling 6 Sound Test.

Main Methods:

  • A case series design was employed at a single tertiary care medical center.
  • Pediatric patients with ANSD confirmed by Auditory Brainstem Response (ABR) testing were included.
  • Audiologic outcomes were assessed using the IT-MAIS and Ling 6 Sound Test for patients with hearing aid use.

Main Results:

  • Ten pediatric patients with ANSD using hearing aids were analyzed.
  • The Infant Toddler-Meaningful Auditory Integration Scale (IT-MAIS) scores improved by an average of 20.4% with hearing aid use.
  • Ling 6 Sound Test scores showed improvement, increasing from an average of 3.6 to 4.8 with amplification.

Conclusions:

  • Hearing aid use generally leads to improved audiologic outcomes in children with ANSD.
  • Both initial and extended hearing aid use demonstrated positive effects on IT-MAIS and Ling 6 scores.
  • Further multi-institutional studies are recommended to investigate long-term impacts and confounding factors.
Abstract

Keywords:
ANSDIT-MAISLing 6 sound test

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