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Budd-Chiari syndrome treated by Senning operation
M J Mahony1, J M Littlewood, M S Losowsky
1Department of Paediatrics, St James's University Hospital, Leeds.
Archives of Disease in Childhood
|June 1, 1988
Summary
Budd-Chiari syndrome, a rare liver condition, was diagnosed in a pediatric patient presenting with ascites. Surgical intervention successfully resolved the ascites, with the patient showing sustained recovery.
Area of Science:
- Hepatology
- Vascular Surgery
- Pediatric Gastroenterology
Background:
- Budd-Chiari syndrome is a rare hepatic vascular disease characterized by hepatic venous outflow obstruction.
- Ascites is a common and challenging manifestation of Budd-Chiari syndrome, significantly impacting patient quality of life.
Observation:
- A 13-year-old male presented with symptomatic ascites, indicative of advanced Budd-Chiari syndrome.
- Angiographic imaging revealed critical occlusion at the ostia of the hepatic veins, confirming the diagnosis.
Findings:
- The patient underwent a Senning operation, involving transcaval liver resection and hepatocaval anastomosis.
- Post-operative assessment showed complete resolution of ascites and a positive clinical outcome.
Implications:
- Surgical management, specifically the Senning procedure, offers a viable treatment option for pediatric Budd-Chiari syndrome with venous occlusion.
- This case highlights the potential for successful surgical correction and long-term recovery in young patients with this complex condition.