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Surgical Treatment of Lutembacher Syndrome with a Huge Right Atrium: A Case Report
Maodong Yang1, Li Zhang2, Han Tang3
1Department of Cardiovascular Surgery, Yan'an Affiliated Hospital of Kunming Medical University, Kunming, China. ymd0468@126.com.
Insights
Lutembacher's syndrome (LS), a rare heart defect combining atrial septal defect (ASD) and mitral stenosis (MS), was successfully treated surgically in a 39-year-old male with a large right atrium.
Area of Science:
- Cardiology
- Cardiovascular Surgery
- Medical Case Reports
Background:
- Lutembacher's syndrome (LS) is a rare cardiovascular anomaly characterized by atrial septal defect (ASD) and mitral stenosis (MS).
- Clinical presentation and hemodynamic impact of LS vary based on the interplay between ASD and MS.
Background:
Lutembacher's syndrome (LS) is a rare cardiovascular anomaly that is defined as any combination of congenital or iatrogenic atrial septal defect (ASD) with congenital or acquired mitral stenosis (MS). The clinical features and hemodynamic effects of LS depend on the balance between ASD and MS.
Case Report:
In this case report, we describe a rare case of LS with a huge right atrium in a 39-year-old male patient who was admitted to the hospital with worsening fatigue and breathlessness on exertion. Clinical examination revealed central cyanosis, raised jugular venous pressure bilaterally, clear breath sounds bilaterally with no dry and wet rales, hyperdynamic apex beat, and dull heart sounds. His vital signs on admission included blood pressure of 90/60 mmHg, irregular pulse of 76 beats/min, and oxygen saturation of 90.4%. Echocardiography revealed moderate to severe MS with ASD (ostium secundum). The patient's condition deteriorated after initial medical management, and he underwent open heart surgery for mitral valve replacement, ASD repair, tricuspid annuloplasty, and right atrial volume reduction.
Conclusions:
This case report describes the successful surgical management of this rare condition.
