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Neutrophil Elastase Defects in Congenital Neutropenia

Zuzanna Rydzynska1, Bartlomiej Pawlik1,2, Damian Krzyzanowski1,3

  • 1Department of Pediatrics, Oncology and Hematology, Medical University of Lodz, Lodz, Poland.

Frontiers in Immunology
|May 10, 2021
PubMed

Keywords:
ELANE mutationscyclic neutropeniamislocalizationmistraffickingneutrophil elastasesevere congenital neutropeniaunfolded protein response

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