HRCT Diagnosis of Pleuroparenchymal fibroelastosis: Report of two cases

Ali Morshid1, Amin Moshksar1, Aparna Das2

  • 1Department of Diagnostic Radiology, University of Texas Medical Branch, Galveston TX 77555.

Insights

Pleuroparenchymal fibroelastosis (PPFE) is a rare lung disease often missed on CT scans. Recognizing CT patterns is crucial for identifying patients who may experience rapid disease progression and clinical decline.

Area of Science:

  • Pulmonology
  • Radiology
  • Pathology

Background:

  • Pleuroparenchymal fibroelastosis (PPFE) is a rare idiopathic interstitial pneumonia.
  • It is characterized by fibrosis of the visceral pleura and subpleural lung parenchyma.
  • PPFE is frequently underdiagnosed on computed tomography (CT) scans.

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