[Current concepts on mucoviscidosis. Report of 2 cases]

The main aspects of the genetic cystic fibrosis, are reviewed; they are: incidence, pathophysiology, clinical signs and symptoms, treatment and prognosis. Emphasis is made on the infrequency of the diagnosis in Latin America. The pediatrician's attention is called in order to think in this possible diagnosis in cases of chronic pneumopathy with or without signs of poor intestinal absorption.