Objective assessment of muscle strength in chronic relapsing dysimmune polyradiculoneuropathy

Chronic, relapsing dysimmune polyradiculoneuropathy is an uncommon disease which occasionally affects children. The relapsing-remitting and/or progressive symptoms may be refractory to treatment. Regular, objective assessment of muscle strength, visually displayed, facilitates knowledge of the natural history of the disease and predicts response to treatment, and thus optimum planning for treatment. Myometry, discussed in this report, appears to be an objective and useful technique for this purpose, as illustrated in two teenage girls with this disease.