Gordon syndrome: Dental implications and a case report

Area of Science:

• Medical Genetics
• Dental Anthropology
• Craniofacial Biology

Background:

• Gordon syndrome is a rare genetic disorder characterized by distinctive craniofacial anomalies.
• Limited mouth opening (trismus) and impaired manual dexterity are common clinical manifestations.
• Dental management for patients with Gordon syndrome requires specialized considerations.

Observation:

• A 14-year-old male with Gordon syndrome presented with severe dental caries and limited mouth opening (2 cm).
• Craniofacial features included low-set ears, down-slanted palpebral fissures, sloping shoulders, and a prognathic mandible.
• Radiographic findings revealed missing and impacted premolars, taurodontism, and enlarged coronoid processes.

Findings:

• The patient exhibited significant dental abnormalities, including extensive caries and agenesis of mandibular premolars.
• Enlarged coronoid processes contributed to the restricted mandibular movement.
• Dental interventions included extractions and restorations under local anesthesia.

Implications:

• Patients with Gordon syndrome require tailored dental care plans to address limited mouth opening and manual dexterity issues.
• Customized homecare strategies and frequent professional dental visits are crucial for maintaining oral hygiene.
• This case highlights the importance of a multidisciplinary approach in managing complex craniofacial and dental conditions.