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Complication of Hirschsprung's disease immediately after pregnancy: A rare case report
William Sergi1, Francesco Serra1, Giovanni Cucciarrè1
1Department of Surgery, University of Modena and Reggio Emilia - Policlinico of Modena, Via del Pozzo, 71, 41100, Modena, Italy.
Insights
Adult Hirschsprung
Area of Science:
- Gastroenterology
- Colorectal Surgery
- Pediatric Surgery
Background:
- Hirschsprung's disease (HD) is a rare congenital colonic disorder.
- Adult-onset HD can lead to severe complications and reduced quality of life.
- Sigmoid volvulus (SV) is an uncommon but critical presentation of HD in adults.
Purpose of the Study:
- To present a case of adult-onset HD presenting as sigmoid volvulus.
- To evaluate the safety and efficacy of surgical management for this condition.
Main Methods:
- A young woman with known HD developed colonic obstruction due to sigmoid volvulus post-childbirth.
- Initial treatment involved Hartmann's procedure.
- Subsequent surgical restoration of digestive continuity was performed using a two-stage Duhamel's procedure.
Main Results:
- The patient's sigmoid volvulus was successfully treated with Hartmann's procedure.
- The two-stage Duhamel's procedure effectively restored digestive continuity without complications.
- The patient achieved a good quality of life post-surgery.
Conclusions:
- Duhamel's procedure is a safe and effective surgical option for adult patients with Hirschsprung's disease.
- Timely surgical intervention can significantly improve quality of life in adult HD patients presenting with complications.
Introduction And Importance:
Hirschprung's disease (HD) is a rare congenital colonic disorder that may develop in adult age, often determining a poor life quality with complications needing an emergency surgical setting. The disease rarely presents as an acute intestinal obstruction like SV, which represents an abdominal emergency issue.
Case Presentation:
A few days after discharge from gynecology unit because of her first childbirth, a young woman with HD developed colonic obstruction due to sigmoid volvulus, which was treated with Hartmann's procedure.
Clinical Discussion:
Some months later, the patient underwent a two-stage Duhamel's procedure to restore the digestive tract's continuity. Both hospital periods were free of critical events.
Conclusion:
The woman regained a good quality of life: Duhamel's procedure revealed as a safe technique to use in HD adult.
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