Complication of Hirschsprung's disease immediately after pregnancy: A rare case report

William Sergi1, Francesco Serra1, Giovanni Cucciarrè1

  • 1Department of Surgery, University of Modena and Reggio Emilia - Policlinico of Modena, Via del Pozzo, 71, 41100, Modena, Italy.

Insights

Adult Hirschsprung

Area of Science:

  • Gastroenterology
  • Colorectal Surgery
  • Pediatric Surgery

Background:

  • Hirschsprung's disease (HD) is a rare congenital colonic disorder.
  • Adult-onset HD can lead to severe complications and reduced quality of life.
  • Sigmoid volvulus (SV) is an uncommon but critical presentation of HD in adults.

Purpose of the Study:

  • To present a case of adult-onset HD presenting as sigmoid volvulus.
  • To evaluate the safety and efficacy of surgical management for this condition.

Main Methods:

  • A young woman with known HD developed colonic obstruction due to sigmoid volvulus post-childbirth.
  • Initial treatment involved Hartmann's procedure.
  • Subsequent surgical restoration of digestive continuity was performed using a two-stage Duhamel's procedure.

Main Results:

  • The patient's sigmoid volvulus was successfully treated with Hartmann's procedure.
  • The two-stage Duhamel's procedure effectively restored digestive continuity without complications.
  • The patient achieved a good quality of life post-surgery.

Conclusions:

  • Duhamel's procedure is a safe and effective surgical option for adult patients with Hirschsprung's disease.
  • Timely surgical intervention can significantly improve quality of life in adult HD patients presenting with complications.
Abstract