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Behcet's disease and multiple arterial aneurysms: 4 case reports.

Javad Salimi1, Zahra Omrani2, Roozbeh Cheraghali3

  • 1Vascular and Endovascular Surgery, Liver Transplantation Program, Tehran University of Medical Sciences, Tehran, Iran.

Journal of Surgical Case Reports
|May 31, 2021
PubMed
Summary

Behcet's disease, a rare vasculitis, can cause multiple aneurysms, including subclavian artery aneurysms. This report details four cases, highlighting diverse surgical and endovascular treatments for these complex vascular conditions.

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Area of Science:

  • Vascular Surgery
  • Rheumatology
  • Internal Medicine

Background:

  • Behcet's disease (BD) is a rare systemic vasculitis of unknown etiology, predominantly affecting populations along the historical Silk Road.
  • While BD is uncommon in Western countries, its association with vascular complications, particularly aneurysms, necessitates careful clinical consideration.

Observation:

  • This report presents four unique cases of Behcet's disease presenting with multiple arterial aneurysms.
  • Three of the four patients exhibited subclavian artery aneurysms, underscoring a potential predilection in this cohort.
  • The diverse clinical presentations mandated individualized surgical strategies for each patient.

Findings:

  • Surgical and endovascular interventions were employed, with endovascular stent grafts utilized in specific cases.

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  • The study facilitates a discussion comparing open surgical versus endovascular treatment modalities for aneurysms associated with Behcet's disease.
  • Implications:

    • This case series expands the understanding of Behcet's disease-related vascular manifestations, particularly aneurysms.
    • It emphasizes the importance of tailored treatment approaches, considering both open and endovascular options for managing complex vascular pathology in BD patients.
    • Further research into optimal management strategies for BD-associated aneurysms is warranted.