Transtemporal planned partial resection of bilateral acoustic neurinomas

In an attempt to overcome the complete auditory deprivation of young patients with bilateral acoustic nerve schwannomas (Morbus v. Recklinghausen) a planned partial resection of the tumour was carried out in 11 hearing ears. The cerebello-pontine angle was exposed by the enlarged middle fossa approach (Wigand et al., HNO 1985). A strip of tumour was left in contiguity to the facial and cochlear nerves. Hearing was initially preserved in all cases. Four of them, however, developed total deafness after 3-39 months. Recurrent tumour growth was checked by CT scans. During the observation time one resting tumour became invisible, five remained unchanged. Two grew larger. Three cases dropped out of the follow-up. With regard to the high value of preserved auditory function during the first decades of life the planned partial resection may be considered preferable for cases of bilateral acoustic neuromas.