[Idiopathic periostal hyperostosis with dysproteinemia (author's transl)]

The idiopathic periostal hyperostosis with dysproteinemia shows typical symptoms: acute onset with high fever and severe pain in the forearms and the praetibial area, periostal reaction along the ulnae and tibiae accompanied by hypalbuminemia and alpha2-globulin increase. The clinical entity has yet been described in only 2 cases. Our own case illustrates the longterm follow-up. The differential diagnosis especially of Caffey-Syndrom is discussed.